{"id":111666,"date":"2026-07-03T12:15:39","date_gmt":"2026-07-03T10:15:39","guid":{"rendered":"https:\/\/www.pcb.ub.edu\/la-investigadora-del-ibmb-csic-elisa-marti-recibe-una-erc-advanced-grant-para-el-estudio-de-la-espina-bifida\/"},"modified":"2026-07-07T10:27:56","modified_gmt":"2026-07-07T08:27:56","slug":"la-investigadora-del-ibmb-csic-elisa-marti-recibe-una-erc-advanced-grant-para-el-estudio-de-la-espina-bifida","status":"publish","type":"post","link":"https:\/\/www.pcb.ub.edu\/es\/la-investigadora-del-ibmb-csic-elisa-marti-recibe-una-erc-advanced-grant-para-el-estudio-de-la-espina-bifida\/","title":{"rendered":"La investigadora del IBMB-CSIC, Elisa Mart\u00ed, recibe una ERC Advanced Grant para el estudio de la espina b\u00edfida"},"content":{"rendered":"<p><strong>Elisa Mart\u00ed, investigadora del Instituto de Biolog\u00eda Molecular de Barcelona (<a href=\"https:\/\/www.pcb.ub.edu\/es\/empresa\/institut-de-biologia-molecular-de-barcelona-ibmb-csic\/\" target=\"_blank\" rel=\"noopener\">IBMB-CSIC<\/a>), situado en el Parque Cient\u00edfico de la Universidad de Barcelona (PCB-UB), ha conseguido una de las nueve ayudas Advanced Grant que otorga el Consejo Europeo de Investigaci\u00f3n (ERC, por sus siglas en ingl\u00e9s), para investigar los mecanismos biol\u00f3gicos que originan la espina b\u00edfida, una de las malformaciones cong\u00e9nitas m\u00e1s frecuentes del sistema nervioso.<\/strong><\/p>\n<p>En esta convocatoria, el Consejo Superior de Investigaciones Cient\u00edficas (CSIC) ha superado su m\u00e1ximo hist\u00f3rico de financiaci\u00f3n en esta categor\u00eda del ERC y es el organismo con m\u00e1s proyectos financiados en Espa\u00f1a.<\/p>\n<h3><strong>Desentra\u00f1ando la espina b\u00edfida<\/strong><\/h3>\n<p>La espina b\u00edfida se produce durante las primeras etapas del desarrollo embrionario y puede provocar importantes secuelas neurol\u00f3gicas, entre ellas la p\u00e9rdida parcial o total de movilidad en las piernas. A pesar de d\u00e9cadas de investigaci\u00f3n, los mecanismos que la originan contin\u00faan sin estar del todo resueltos.<\/p>\n<p>El proyecto <em>SpinaLogic<\/em>, liderado por <strong>Elisa Mart\u00ed<\/strong>, estudiar\u00e1 c\u00f3mo determinadas mutaciones gen\u00e9ticas identificadas en pacientes con espina b\u00edfida afectan al desarrollo temprano de la m\u00e9dula espinal. Para ello, el equipo introducir\u00e1 estas mutaciones en modelos experimentales de m\u00e9dula espinal humana generados en el laboratorio, con el objetivo de comprender c\u00f3mo las alteraciones gen\u00e9ticas modifican el comportamiento de las c\u00e9lulas durante la formaci\u00f3n del tubo neural, la estructura embrionaria que dar\u00e1 lugar a la m\u00e9dula espinal.<\/p>\n<p>Esta aproximaci\u00f3n permitir\u00e1 establecer, por primera vez, una conexi\u00f3n directa entre las mutaciones gen\u00e9ticas asociadas a la enfermedad y los procesos celulares que tienen lugar durante el desarrollo embrionario humano, lo que ayudar\u00e1 a entender mejor c\u00f3mo se origina.<\/p>\n<p>\u201cPosarem a prova una hip\u00f2tesi nova: que els problemes de mobilitat que presenten molts pacients podrien deure, almenys en part, a una producci\u00f3 insuficient de neurones motores durant les etapes m\u00e9s primerenques de formaci\u00f3 de la medul\u00b7la espinal\u201d, exposa <strong>Mart\u00ed<\/strong>. \u201cConfirmar aquesta idea obriria noves vies per comprendre les seq\u00fceles de la malaltia i, en el futur, explorar possibles estrat\u00e8gies terap\u00e8utiques\u201d, afegeix la investigadora.<\/p>\n<p><em>SpinaLogic<\/em> se apoya en d\u00e9cadas de investigaci\u00f3n sobre los mecanismos que regulan el desarrollo embrionario de la m\u00e9dula espinal, llevada a cabo principalmente en modelos animales. Gracias a este conocimiento previo, el equipo ha desarrollado organoides \u2014peque\u00f1as estructuras tridimensionales obtenidas a partir de c\u00e9lulas madre\u2014 que reproducen con gran fidelidad las primeras etapas del desarrollo de la m\u00e9dula espinal humana.<\/p>\n<p>Utilizando estos organoides, el equipo introducir\u00e1 las mutaciones identificadas en pacientes con espina b\u00edfida para estudiar, por primera vez en un modelo humano experimental, las bases biol\u00f3gicas de esta malformaci\u00f3n cong\u00e9nita. El proyecto combina gen\u00e9tica humana, biolog\u00eda del desarrollo y tecnolog\u00edas avanzadas de organoides para abordar una cuesti\u00f3n que sigue sin respuesta pese a d\u00e9cadas de investigaci\u00f3n.<\/p>\n<p>Desde 2001, <strong>Elisa Mart\u00ed<\/strong> lidera su grupo de investigaci\u00f3n independiente en el IBMB-CSIC, reconocido internacionalmente por sus trabajos en redes gen\u00e9ticas y procesos celulares que regulan el desarrollo neural.<\/p>\n<p><strong>\u00bb Enlace a la noticia: <\/strong><a href=\"https:\/\/delegacion.catalunya.csic.es\/el-csic-obtiene-nueve-advanced-grant-del-erc-dos-de-ellas-en-la-imf-y-el-ibmb-en-cataluna\/?lang=ca\" target=\"_blank\" rel=\"noopener\">web del CSIC Catalunya [+]<\/a><\/p>\n","protected":false},"excerpt":{"rendered":"<p>Elisa Mart\u00ed, investigadora del Instituto de Biolog\u00eda Molecular de Barcelona (IBMB-CSIC), situado en el Parque Cient\u00edfico de la Universidad de Barcelona (PCB-UB), ha conseguido una de las nueve ayudas Advanced&#8230;<\/p>\n","protected":false},"author":14,"featured_media":111664,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"inline_featured_image":false,"footnotes":""},"categories":[113],"tags":[334],"class_list":["post-111666","post","type-post","status-publish","format-standard","has-post-thumbnail","category-entidades","tag-ibmb-es"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.0 - 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